A neurofibromatosis plexiform neurofibroma (NF1-PN) can grow on any group of nerves in the body.
What Is a Neurofibroma?
A nerve plexus is a branching web link of nerves.
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Neurofibromas are tumors that affect a nerve plexus.
The complications of these tumors are determined by their location.
Sometimes, an NF1-PN can prevent a child from developing the skills controlled by the affected nerves.
While NF1-PN tumors are usually benign, in rare instances, they can become malignant (cancerous).
The condition itself may change with an increasing number of growths and tumors.
Usually, benign tumors, such as NF1-PN, are not fatal.
However, benign tumors can be life-threatening if they compress vital body structures.
Some NF1 tumors are malignant and can spread and invade the tissues and organs throughout the body.
Malignant tumors have a high risk of being life-threatening.
Approximately 8% to 13% of people who have NF1 are diagnosed with a malignant tumor.
Inoperable Tumors
Some tumors can be removed surgically while many others cannot due to their location.
This prescription medication is taken twice daily.
A pain management physiciancan often provide interventional procedures to help manage pain.
A physical therapist can work with you to help you optimize your physical mobility and abilities.
A dermatologist can examine your skin growths and discoloration and prescribe treatment, if necessary.
An oncologist can provide surveillance and treatment of tumors.
Side Effects of Koselugo (selumetinib)
This medication can be beneficial for children who have NF1-PN.
Side effects can include:
Summary
Living with NF1 can significantly impact your life.
This condition begins during childhood and affects the skin and nervous system.
Plexiform neurofibromas (PN) are a throw in of tumor that can grow in the nervous system.
These tumors can often be treated surgically.
doi:10.7759/cureus.23141
National Institute of Neurological Disorders and Stroke.Neurofibromatosis.
