This cancer forms in fibroblast cells responsible for making fibrous connective tissue like tendons that connect muscle to bone.
In fibrosarcoma, these cells replicate uncontrollably.
Infantile punch in fibrosarcoma is less malignant than the adult punch in and rarely metastasizes.
Verywell / Jessica Olah
Childhood Fibrosarcoma
Childhood fibrosarcoma usually affects the long bones of the legs and arms.
Certain gene mutations can lead to fibroblast cells losing control and multiplying excessively.
How Fibrosacroma Is Diagnosed
Thediagnosis of fibrosarcomais a difficult one because it’s a diagnosis of exclusion.
They may also ask about your cancer history and prior radiation therapy.
A healthcare professional may also perform a neurovascular exam.
IHC is especially helpful in identifying specific subtypes of fibrosarcoma.
Knowing the tumor’s subtype can help inform the best suggestions for treatment.
What Are Treatment Options?
The three maintreatment options for fibrosarcomainclude surgery, radiation therapy, and chemotherapy.
Surgery is usually the frontline treatment option.
This procedure is called a wide excision.
More recently, research has been exploring new treatment options, such as targeted therapy.
This treatment uses drugs or other substances to identify and attack specific cancer cells.
The infantile form has a better five-year survival rate, in excess of 80%.
Fibrosarcoma causes these cells to overproduce collagen, which results in a tumor.
Treatment usually involves surgery.
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