It is the second most common jot down ofhemophiliaand occurs in approximately 1 in 25,000 male births.
Factor IX is a blood-clotting factor that promotes healing and helps the body seal wounds.
As a result, people who have hemophilia B bruise easily and bleed for longer periods of time.
Verywell / Theresa Chiechi
Other names for hemophilia B, include factor IX deficiency, Christmas disease, and the royal disease.
Types of Hemophilia
There are many factors involved in the process of forming a blood clot.
The jot down ofhemophiliathat you might have is based on which blood clotting factor you are deficient in.
Insufficient levels of factor VIII, factor IX, and factor XI are most common.
The three main forms of hemophilia are:
What Are the Symptoms?
Symptoms of hemophilia are largely dependent on the amount of factor IX (FIX) in your blood.
Some people may not experience their first episode until adulthood, while others notice symptoms during infancy or childhood.
Generally, the higher your levels of FIX, the milder your symptoms will be.
Women with mild hemophilia often experienceheavy menstrual bleeding(previously calledmenorrhagia) and canhemorrhageafter childbirth.
Even a small amount of FIX can stave off life-threatening bleeding episodes.
Causes and Risk Factors
Hemophilia B is a hereditary disease.
Hemophilia B is due to defects in the F9 gene located on the X chromosome.
The F9 gene is just one gene involved in the blood-clotting process.
It is responsible for manufacturing and activating factor IX.
Specialized blood coagulation tests are needed to confirm the diagnosis.
Blood tests are used to measure how long it takes your blood to form a clot.
What Are the Treatment Options?
There are two types of clotting factor concentrates that may be given intravenously (via IV, intravenously).
These include:
Hemophilia treatments are often given at a comprehensive hemophilia treatment center (HTC).
This one-time infusion increases circulating Factor IX in the blood.
Summary
Hemophilia B is a hereditary condition that can cause minor and major bleeding episodes.
The condition is due to a deficiency in blood-clotting factor called factor IX.
This condition can be diagnosed with blood tests.
Some people with hemophilia experience frequent bleeding episodes, while others experience very few.
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